Gastrointestinal Manifestations of Cystic Fibrosis

Radiologic-Pathologic Correlation

Abstract Introduction Intestinal Obstruction and Its Complications Nonobstructive Bowel Manifestations

Pancreatic Abnormalities Hepatobiliary Abnormalities CF and Gastrointestinal Malignancy

Prognosis and Future Perspectives Summary Source Information References

References

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Return to: Introduction | Pancreatic Abnormalities | Hepatobiliary Abnormalities

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48. Holsclaw D, Rocmans C, Shwachman H. Intussusception in patients with cystic fibrosis. Pediatrics 1971; 48:51-58.
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53. Kirks DR. Air intussusception reduction: "the winds of change." Pediatr Radiol 1995; 25:89-91.
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55. Zerin JM, Kuhn-Fulton J, White SJ, et al. Colonic strictures in children with cystic fibrosis. Radiology 1995; 194:223-226.
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58. Campbell CA, Forrest J, Musgrove C. High-strength pancreatic enzyme supplements and large-bowel stricture in cystic fibrosis (letter; comment). Lancet 1994; 343:109-110.
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68. Taussig LM, Saldino RM, di Sant Agnes PA. Radiographic abnormalities of the duodenum and small bowel in cystic fibrosis of the pancreas (mucoviscidosis). Radiology 1973; 106:369-376.
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69. Berk RN, Lee FA. The late gastrointestinal manifestations of cystic fibrosis of the pancreas. Radiology 1973; 106:377-381.
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Return to: Pancreatic Abnormalities

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96. Lindblad A, Hultcrantz R, Strandvik B. Bile-duct destruction and collagen deposition: a prominent ultrastructural feature of the liver in cystic fibrosis. Hepatology 1992; 16:372-381.
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111. Roy CC, Weber AM, Morin CL, et al. Abnormal biliary lipid composition in cystic fibrosis: effect of pancreatic enzymes. N Engl J Med 1977; 297:1301-1305.
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113. Lane JI, Sacks D, Winn RS, Kershner MS. A false-positive hepatobiliary scan in a patient with cystic fibrosis. Clin Nucl Med 1988; 13: 331-333.
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114. Snyder CL, Ferrell KL, Saltzman DA, Warwick WJ, Leonard AS. Operative therapy of gallbladder disease in patients with cystic fibrosis. Am J Surg 1989; 157:557-561.
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115. Neglia JP, FitzSimmons SC, Maisonneuve P, et al. The risk of cancer among patients with cystic fibrosis. N Engl J Med 1995; 332:494-499.
Return to: CF and Gastrointestinal Malignancy

116. Swinson CM, Slavin G, Coles EC, Booth CC. Coeliac disease and malignancy. Lancet 1983; 1:111-115.
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117. FitzSimmons S. Cystic fibrosis foundation patient registry, 1994 annual data report. Bethesda, Md: Cystic Fibrosis Foundation, 1995.
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118. Mack DR, Traystman MD, Colombo JL, et al. Clinical denouement and mutation analysis of patients with cystic fibrosis undergoing liver transplantation for biliary cirrhosis. J Pediatr 1995; 127:881-887.
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122. Highlights: selected proceedings from the 8th annual North American Cystic Fibrosis Conference. New York, NY: Wiley-Liss, 1994.
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Abstract Introduction Intestinal Obstruction and Its Complications Nonobstructive Bowel Manifestations

Pancreatic Abnormalities Hepatobiliary Abnormalities CF and Gastrointestinal Malignancy

Prognosis and Future Perspectives Summary Source Information References